Table 2 Spectrum and frequency of clinical diagnoses in patients with RPD.

From: The evolving etiologies of rapidly progressive dementia: a systematic review

Etiological categories

n

%

NDD

459

27.0%

AD

214

12.6%

FTD

110

6.5%

DLB

67

3.9%

NIID

5

0.3%

Other NDD

63

3.7%

VaD

95

5.6%

CJD

214

12.6%

NPH

23

1.4%

CNS infections

295

17.3%

Virus encephalitis

87

5.1%

Neurocysticercosis

66

3.9%

Neurosyphilis

64

3.8%

HIV infection

11

0.6%

Other infections

67

3.9%

Neuroimmune diseases

327

19.2%

AE

266

15.6%

CNS vasculitis

26

1.5%

CNS demyelinating disease

16

0.9%

Other inflammatory disorders

19

1.1%

Intracranial tumors

67

3.9%

Metabolic/toxic diseases

95

5.6%

Hereditary diseases

12

0.7%

CAA-RI

8

0.5%

Others

106

6.2%

  1. AD Alzheimer’s disease, AE autoimmune encephalitis, CAA-RI cerebral amyloid angiopathy-related inflammation, CJD Creutzfeldt-Jakob disease, CNS central nervous system, DLB dementia with Lewy bodies, FTD frontotemporal dementia, HIV human immunodeficiency virus, NDD neurodegenerative disease, NIID neuronal intranuclear inclusion disease, NPH normal pressure hydrocephalus, RPD rapidly progressive dementia, VaD vascular dementia.