Table 2 Spectrum and frequency of clinical diagnoses in patients with RPD.
From: The evolving etiologies of rapidly progressive dementia: a systematic review
Etiological categories | n | % |
|---|---|---|
NDD | 459 | 27.0% |
AD | 214 | 12.6% |
FTD | 110 | 6.5% |
DLB | 67 | 3.9% |
NIID | 5 | 0.3% |
Other NDD | 63 | 3.7% |
VaD | 95 | 5.6% |
CJD | 214 | 12.6% |
NPH | 23 | 1.4% |
CNS infections | 295 | 17.3% |
Virus encephalitis | 87 | 5.1% |
Neurocysticercosis | 66 | 3.9% |
Neurosyphilis | 64 | 3.8% |
HIV infection | 11 | 0.6% |
Other infections | 67 | 3.9% |
Neuroimmune diseases | 327 | 19.2% |
AE | 266 | 15.6% |
CNS vasculitis | 26 | 1.5% |
CNS demyelinating disease | 16 | 0.9% |
Other inflammatory disorders | 19 | 1.1% |
Intracranial tumors | 67 | 3.9% |
Metabolic/toxic diseases | 95 | 5.6% |
Hereditary diseases | 12 | 0.7% |
CAA-RI | 8 | 0.5% |
Others | 106 | 6.2% |