Table 1 Clinical characteristics of 30 DSRCT patients

From: Multi-layered molecular profiling informs the diagnosis and targeted therapy of desmoplastic small round cell tumor

Age at enrollment (years)

 

Median

30

Range

18–56

Age at diagnosis (years)

 

Median

27

Range

18–55

Sex

 

Male

n  =  26 (86.7%)

Female

n  =  4 (13.3%)

Primary tumor site

 

Intra-abdominal

n  =  27 (90%)

Extra-abdominal

n  =  3 (10%)

Metastatic disease at diagnosis

 

Yes

n  =  23 (76.7%)

No

n  =  7 (23.3%)

Metastatic site at diagnosis

 

Lymph nodes

n  =  18 (60%)

Liver

n  =  10 (33.3%)

Lung

n  =  7 (23.3%)

Bone

n  =  5 (16.7%)