Table 1 Demographic and clinical characteristics at presentation of patients with primary FSGS (N = 8).

From: Management and long-term outcome of recurrent idiopathic FSGS in pediatric kidney transplant recipients

Variable

 

Sex - N (%)

 

Female

3 (37.5%)

Male

5 (62.5%)

Ethnicity - N (%)

 

Arab/Moslem

6 (75%)

Arab/Christian

1 (12.5%)

Jewish

1 (12.5%)

Primary histopathology - N (%)

 

FSGS

4 (50%)

MCD

3 (37.5%)

Unknown

1 (12.5%)

Age at presentation, years

 

Median

6

Average (SD)

7 (4.75)

Primary steroid sensitivity - N (%)

 

Yes

3 (37.5%)

No

5 (62.5%)

Genetic testing - N (%)

 

Yes, negative results

7 (87.5%)

No

1 (12.5%)

Time to kidney failure, years

 

Median

3

Average (SD)

4.3 (4.2)

Donor source - N (%)

 

Living related donor

3 (37.5%)

Deceased donor

5 (62.5%)

Preemptive PP - N (%)

 

Yes

5 (62.5%)

No

3 (37.5%)

Induction protocol - N (%)

 

Basiliximab + corticosteroids

7 (87.5%)

Thymoglobulin + corticosteroids

1 (12.5%)

Delayed Graft function - N (%)

 

Yes

3 (37.5%)

No

5 (62.5%)

Maintenance drug regimen - N (%)

 

MMF + Tacrolimus + steroids

8 (100%)

rFSGS - N (%)

 

Yes

6 (75%)

No

2 (25%)

Time to recurrence, days

 

Median

2.5

Average (SD)

12.5 (23)