Fig. 4: Complex heterotaxy syndrome with left atrial isomerism in an 11-year-old male patient from Azerbaijan, with a history of post-Kawashima procedure for interrupted IVC with azygos continuation, double-outlet right ventricle, residual pulmonary artery stenosis, and complete atrioventricular septal defect. | Communications Medicine

Fig. 4: Complex heterotaxy syndrome with left atrial isomerism in an 11-year-old male patient from Azerbaijan, with a history of post-Kawashima procedure for interrupted IVC with azygos continuation, double-outlet right ventricle, residual pulmonary artery stenosis, and complete atrioventricular septal defect.

From: Applying artificial intelligence to cardiac MRI to diagnose congenital heart disease in low-resource settings such as Sub-Saharan Africa

Fig. 4

The clinical course was complicated by right pleural effusions and ascites. Cardiac catheter angiography failed to cannulate the previously placed Dacron graft, raising suspicion of graft thrombosis. CMR revealed thrombotic occlusion of the Dacron graft (asterisks; a, c), a large AVSD (arrow; a, b) and pleural effusion (E; a, c), together with significant narrowing of the right pulmonary artery and restricted flow toward the right lung. AVSD atrioventricular septal defect, CMR cardiac magnetic resonance imaging, E effusion, IVC inferior vena cava, L-SVC left superior vena cava, RPA right pulmonary artery, R-SVC right superior vena cava.

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